Neurological Surgery 脳神経外科34巻1号

2006年01月発行

症例

脈絡叢乳頭腫/乳頭癌7例の検討

著者： 野下展生¹ 隈部俊宏¹ 嘉山孝正² 冨永悌二¹

所属機関： ¹東北大学大学院神経外科学分野 ²山形大学医学部脳神経外科

ページ範囲：P.73 - P.81

Ⅰ．は じ め に

　脈絡叢乳頭腫/乳頭癌（choroid plexus tumor: CPT）は全頭蓋内腫瘍の0.4～1.0%程度といわれる稀な腫瘍である^3,15,22,24)．その好発年齢は2歳以下が全体の70%を占めると報告されており^3,5)，小児に多い^8,11,25)．好発部位は小児と成人で異なり，小児では側脳室，成人では第4脳室で多い²⁵⁾．脳室内に発生することがほとんどだが，稀に脳室外発生も報告されている^12,19)．治療に関しては，手術による全摘出の可否が予後にかかわるといわれるが^5,8,18,25)，補助療法については議論が分かれている．これまで単一施設での治療成績についてはいくつか報告があるが^{2,3,6,8,13,15,16,18,22)}，日本国内においては症例報告を散見するにとどまる^12,14)．本稿では当施設においてMRI導入以降の1989年より治療したCPT 7症例の臨床経過について検討し，過去の文献的考察を加えて報告する．

参考文献

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