Neurological Surgery 脳神経外科51巻5号

2023年09月発行

特集 臨床脳神経外科医にとってのWHO脳腫瘍分類第5版 Ⅳ 小児脳腫瘍

限局性星細胞系膠腫

著者： 林弘明¹ 岩下広道² 立石健祐³⁴

所属機関： ¹横浜市立大学大学院医学研究科発生成育小児医療学 ²横浜市立大学大学院医学研究科病態病理学 ³横浜市立大学大学院医学研究科脳神経外科学 ⁴横浜市立大学大学院生命医科学研究科創薬再生科学研究室

ページ範囲：P.884 - P.891

Point
・WHO脳腫瘍分類第5版では，新たに限局性星細胞系膠腫が加わった．
・限局性星細胞系膠腫には，毛様細胞性星細胞腫，多形黄色星細胞腫をはじめとする6つの腫瘍型が含まれる．
・限局性星細胞系膠腫の多くでMAPK経路の遺伝子異常が認められる．

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