文献詳細
文献概要
今月の主題 骨髄増殖性疾患 話題
骨髄増殖性疾患と血栓・止血
著者: 横山健次1
所属機関: 1慶應義塾大学医学部血液内科
ページ範囲:P.304 - P.308
文献購入ページに移動1.はじめに
骨髄増殖性疾患(myeloproliferative disorder;MPD)では血栓症の発症頻度が高くなることが報告されている.一方で皮下出血などの出血症状もしばしばみられる症状である.なかでも真性多血症(polycythemia vera;PV),本態性血小板血症(essential thrombocythemia;ET)では血栓症は主要な死因であり,予後を左右する.本稿ではPV,ET患者を中心に,血栓症,出血症状の頻度,成因,治療法などに関して解説する.
骨髄増殖性疾患(myeloproliferative disorder;MPD)では血栓症の発症頻度が高くなることが報告されている.一方で皮下出血などの出血症状もしばしばみられる症状である.なかでも真性多血症(polycythemia vera;PV),本態性血小板血症(essential thrombocythemia;ET)では血栓症は主要な死因であり,予後を左右する.本稿ではPV,ET患者を中心に,血栓症,出血症状の頻度,成因,治療法などに関して解説する.
参考文献
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