臨床検査62巻9号

2018年09月発行

今月の特集2 知っておきたい遺伝性不整脈

カテコラミン感受性多形性心室頻拍（CPVT）

著者： 渡部裕¹ 南野徹¹

所属機関： ¹新潟大学大学院医歯学総合研究科循環器内科学

ページ範囲：P.1072 - P.1079

Point

●カテコラミン感受性多形性心室頻拍（CPVT）は，交感神経活性を高める精神的ないしは肉体的なストレスにより心室頻拍を発症して，突然死をきたしうる．

●遺伝性不整脈のなかでも，CPVTは極めて致死性の高い疾患である．

●運動ないしはカテコラミン刺激によって誘発される多源性の心室性期外収縮，二方向性心室頻拍や多形性心室頻拍によって診断される．

●致死性が高いために，ストレス回避のための生活制限とβ遮断薬を中心とした薬物療法が，全ての症例において推奨される．

参考文献

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