胃と腸38巻4号

2003年04月発行

特集 全身性疾患と消化管病変 総論

1. 消化管疾患にみられる他臓器病変

著者： 大島忠之¹ 横山善文¹ 伊藤恵介¹ 谷田諭史¹ 片岡洋望¹ 佐々木誠人¹ 佐野仁¹ 妹尾恭司¹ 大原弘隆¹ 城卓志¹ 伊藤誠¹ 森田明理²

所属機関： ¹名古屋市立大学大学院臨床機能内科学 ²名古屋市立大学大学院加齢・環境皮膚科学

ページ範囲：P.415 - P.426

　消化管疾患では消化管自体の病変のみならず，消化管以外の他臓器にも特有な病変を発現することがある．これら消化管外病変は，消化管病変より先行して発見されることも多く，消化管疾患に併存・合併する他臓器病変を理解しておくことは臨床上重要である．なかでも内臓病変に合併する皮膚病変はデルマドロームと言われ，日常臨床でしばしば遭遇するので重要な概念である．本稿では，家族性大腸腺腫症，Gardner症候群，Turcot症候群，Peutz-Jeghers症候群，Cronkhite-Canada症候群，Cowden病，潰瘍性大腸炎，Crohn病，腸管Behçet病，Wipple病に合併する他臓器病変を中心に概説した．

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