胃と腸59巻7号

2024年07月発行

今月の主題 虚血性腸病変を整理する

主題

血管炎による虚血性腸病変の病理診断

著者： 宮崎龍彦¹

所属機関： ¹岐阜大学医学部附属病院病理部

ページ範囲：P.927 - P.942

文献概要

要旨●腸の虚血性疾患において，血管炎の占める割合は少なくない．全身性血管炎症候群である結節性多発動脈炎（PAN）やANCA関連血管炎，IgA血管炎，Behçet病などの部分症状としてみられることもあれば，IMHMV（idiopathic myointimal hyperplasia of mesenteric veins）やMIVOD（mesenteric inflammatory veno-occlusive disease），IMP（idiopathic mesenteric phlebosclerosis）などの腸管に限局した病変もまれながら存在する．さらに血管炎類縁疾患として，分節性動脈中膜融解症（SAM）や線維筋性異形成（FMD），抗リン脂質抗体症候群（APS）などもみられる．

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