BRAIN and NERVE－神経研究の進歩66巻12号

2014年12月発行

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特集 Orthopaedic Neurology—神経内科と整形外科の狭間で

神経痛性筋萎縮症

著者： 福島和広¹ 池田修一²

所属機関： ¹信州大学医学部附属病院難病診療センター ²信州大学医学部脳神経内科，リウマチ・膠原病内科

ページ範囲：P.1421 - P.1428

神経痛性筋萎縮症は片側上肢の神経痛で発症し，疼痛の軽快後に肩甲上腕部を中心とした限局性筋萎縮を生じる疾患である。腕神経叢上部とその近傍を首座とする特発性末梢神経障害と考えられており，感染や外傷，労作，遺伝性素因などの誘因が知られる。典型例のほかに，遠位筋優位例や前骨間・後骨間神経麻痺，腰仙神経叢障害など，多様な臨床亜型が知られる。運動機能予後は必ずしも良好ではないが，治療法は確立されていない。

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