BRAIN and NERVE－神経研究の進歩66巻9号

2014年09月発行

総説

マルキアファーヴァ・ビニャミ病の画像診断

著者： 黒田岳志¹ 河村満¹

所属機関： ¹昭和大学医学部内科学講座神経内科学部門

ページ範囲：P.1079 - P.1088

文献概要

マルキアファーヴァ・ビニャミ病はアルコール多飲者に生ずる脳梁の脱髄壊死を特徴とする稀な疾患である。確定診断には剖検が必須であったが，画像診断技術の進歩は生前診断を可能にした。脳梁病変の分布はさまざまで，時に脳梁外病変を伴い，アルコール非乱用者にも生じうることがわかった。今後，画像所見とともに臨床症状や病理所見を併せて検討していくことは，病態の解明および治療法の確立に寄与すると思われる。

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